Abstract
Pulmonary arteriovenous malformations are potentially life-threatening abnormalities that can be exacerbated by pregnancy physiology. Despite prenatal optimization, patients with hereditary hemorrhagic telangiectasia and associated vascular abnormalities continue to experience significant maternal morbidity. Currently, there is a paucity of clinical guidance for managing obstetric patients affected by pulmonary arteriovenous malformations. This case exemplifies the potential to minimize maternal-fetal morbidity and mortality by managing pregnancies affected by pulmonary arteriovenous malformations with a proactive and multidisciplinary approach. Developing an emergency action plan eases decision-making in critical circumstances, allowing for timely intervention. Diagnostic testing for hereditary hemorrhagic telangiectasia and/or pulmonary arteriovenous malformations should be pursued in all at-risk individuals to afford optimization of outcomes. Although this case describes an overall positive outcome, additional research is still needed to help improve maternal and fetal outcomes.