Home > Medical Research Archives > Issue 149 > Pleuroparenchymal Fibroelastosis and Hypersensitivity Pneumonitis: A Clinical, Radiological and Pathological Overview
Published in the Medical Research Archives
Jul 2022 Issue
Pleuroparenchymal Fibroelastosis and Hypersensitivity Pneumonitis: A Clinical, Radiological and Pathological Overview
Published on Jul 31, 2022
DOI
Abstract
Non-idiopathic pleuroparenchymal fibroelastosis (PPFE) has been increasingly reported in the literature. Little is known about the clinical relevance of PFFE and hypersensitivity pneumonitis (HP) overlap; therefore, we sought to investigate the clinical, radiological, and pathological features of patients with these two diseases. Five patients were identified, and the detailed characterization of these cases revealed a heterogeneous group in terms of clinical and treatment options. No mortality, acute exacerbations, or a significant decline in lung function were verified. Our cases seem to have a more “benign” disease behavior, contrary to previous idiopathic PPFE studies. More studies are needed to corroborate these findings and to better elucidate the clinical significance of PPFE and HP overlap.
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