Abstract
Creutzfeldt-Jakob disease (CJD) is a rare neurodegenerative disease of undetermined etiology, In Creutzfeldt-Jakob syndrome the symptomatology is quite variable and it consist of predominantly progressive dementia with a rapid onset, myoclonus, and also cerebellar, pyramidal, extrapyramidal and visual signs, the evolution of this disease is uniformly fatal, most patients die within 12 months, we present a case of a 72 year old women, who was admitted for a status epilepticus, She was later diagnosed with sporadic CJD.